Hematology · Hematology / Lymphoproliferative disorders
Richter syndrome
also: Transformation of chronic lymphocytic leukemia
Transformation of CLL into aggressive lymphoma.
- Specialty
- Hematology
- Subspecialty
- Hematology / Lymphoproliferative disorders
- Sex & age distribution
- Male: affected; Female: affected; Children: no
- Gene(s) involved
- CDKN2A, NOTCH1, TP53
- Alternative names & eponyms
- Transformation of chronic lymphocytic leukemia
Etiology & mechanism
Clonal evolution.
Gene(s) involved (3)
Symptoms & signs (4)
In plain terms, someone with Richter syndrome may experience the following — click any to explore related syndromes:
Same gene(s)
Other syndromes that involve one of this syndrome's genes.
Overlapping symptoms
Other syndromes that share symptoms with this one.
Drag nodes, scroll to zoom, click a node to open that syndrome.
Shares symptoms with
2 shared
Acquired immunodeficiency syndrome
fever, weight loss
2 shared
Stauffer syndrome
fever, weight loss
1 shared
Acute chest syndrome
fever
1 shared
Allan–Herndon–Dudley syndrome
weight loss
1 shared
Antisynthetase syndrome
fever
1 shared
Behçet-like haploinsufficiency of A20 syndrome
fever
1 shared
Blind loop syndrome
weight loss
1 shared
Boerhaave syndrome
fever
1 shared
Cannabinoid hyperemesis syndrome
weight loss
1 shared
Castleman syndrome
fever
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