Variable-vessel vasculitis with recurrent oral and genital ulcers and uveitis.
- Specialty
- Rheumatology
- Subspecialty
- Rheumatology / Vasculitis
- Sex & age distribution
- Male: affected, more severe; Female: affected; Children: yes, rare
- Gene(s) involved
- CCR1, ERAP1, HLA-B*51, IL10, IL12A, IL23R, STAT4
- Alternative names & eponyms
- Behçet disease; Silk Road disease
Etiology & mechanism
Autoinflammatory-autoimmune process with HLA-B51 link.
Gene(s) involved (7)
Symptoms & signs (8)
In plain terms, someone with Behçet syndrome may experience the following — click any to explore related syndromes:
Same gene(s)
Other syndromes that involve one of this syndrome's genes.
Overlapping symptoms
Other syndromes that share symptoms with this one.
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Shares symptoms with
2 shared
Behçet-like haploinsufficiency of A20 syndrome
arthritis, genital ulcers
2 shared
Haploinsufficiency of A20 syndrome
arthritis, genital ulcers
1 shared
Antiphospholipid syndrome
venous thrombosis
1 shared
Antisynthetase syndrome
arthritis
1 shared
Blau syndrome
uveitis
1 shared
Caplan syndrome
arthritis
1 shared
Chilblain lupus syndrome
arthritis
1 shared
Ekbom syndrome
skin lesions
1 shared
Heerfordt syndrome
uveitis
1 shared
Löfgren syndrome with neurological involvement
arthritis
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