Pulmonology · Pulmonology / Pulmonary vascular disease
Portopulmonary hypertension syndrome
also: Portopulmonary syndrome
Pulmonary arterial hypertension in portal hypertension.
- Specialty
- Pulmonology
- Subspecialty
- Pulmonology / Pulmonary vascular disease
- Sex & age distribution
- Male: affected; Female: affected, female predominance; Children: rare
- Gene(s) involved
- BMPR2
- Alternative names & eponyms
- Portopulmonary syndrome
Etiology & mechanism
Vasoconstriction and remodeling from portal circulation mediators.
Gene(s) involved (1)
Symptoms & signs (5)
In plain terms, someone with Portopulmonary hypertension syndrome may experience the following — click any to explore related syndromes:
Same gene(s)
Other syndromes that involve one of this syndrome's genes.
Overlapping symptoms
Other syndromes that share symptoms with this one.
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Shares symptoms with
3 shared
Cardiorenal syndrome
dyspnea, edema, fatigue
3 shared
Eisenmenger syndrome
dyspnea, fatigue, syncope
3 shared
Takotsubo cardiomyopathy
chest pain, dyspnea, syncope
2 shared
Carcinoid heart disease
edema, fatigue
2 shared
Castleman syndrome
edema, fatigue
2 shared
Hughes–Stovin syndrome
chest pain, dyspnea
2 shared
Kounis syndrome
chest pain, dyspnea
2 shared
Lutembacher syndrome
dyspnea, fatigue
2 shared
Microvascular angina
dyspnea, fatigue
2 shared
Middle lobe syndrome
chest pain, dyspnea
Shares genes with
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