Sézary syndrome

Also known as: Cutaneous T-cell lymphoma, leukemic phase

Leukemic cutaneous T-cell lymphoma with erythroderma.

Medical specialty: Hematology
Subspecialty: Hematology / Lymphoproliferative disorders
Sex & age distribution: Male: affected; Female: affected; Children: no
Gene(s) involved: None recorded

Etiology & mechanism

Malignant clonal CD4 T cells.

Gene(s) involved (0)

No gene recorded.

Symptoms & signs (4)

circulating sezary cellserythrodermaintense prurituslymphadenopathy

SyndromeScope — educational reference. Content is model-generated and not clinically verified; always confirm against OMIM, Orphanet and GeneReviews before clinical use.