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Syndrome reference sheet
Generated 12 Oct 2026
Neurology · Neurology / Autonomic disorders

Pourfour du Petit syndrome

Also known as: Reverse Horner syndrome

Mydriasis, eyelid retraction and hyperhidrosis from sympathetic irritation.

Medical specialty
Neurology
Subspecialty
Neurology / Autonomic disorders
Sex & age distribution
Male: affected; Female: affected; Children: rare
Gene(s) involved
None recorded

Etiology & mechanism

Irritative lesion of the cervical sympathetic chain.

Gene(s) involved (0)

No gene recorded.

Symptoms & signs (4)

exophthalmoseyelid retractionhyperhidrosismydriasis
SyndromeScope — educational reference. Content is model-generated and not clinically verified; always confirm against OMIM, Orphanet and GeneReviews before clinical use.