Posterior cortical atrophy

Also known as: Benson syndrome; PCA

Neurodegenerative syndrome with progressive visual-spatial and perceptual dysfunction.

Medical specialty: Neurology
Subspecialty: Neurology / Behavioral neurology; Neuro-ophthalmology
Sex & age distribution: Male: affected; Female: affected, somewhat more common in women; Children: no, onset usually 50–65
Gene(s) involved: None recorded

Etiology & mechanism

Most often Alzheimer pathology in occipito-parietal cortex.

Gene(s) involved (0)

No gene recorded.

Symptoms & signs (6)

alexiabálint featuresgerstmann featurespreserved memory earlysimultanagnosiavisual disorientation

SyndromeScope — educational reference. Content is model-generated and not clinically verified; always confirm against OMIM, Orphanet and GeneReviews before clinical use.