Mounier-Kuhn syndrome

Also known as: Tracheobronchomegaly

Marked tracheal and main bronchial dilation.

Medical specialty: Pulmonology
Subspecialty: Pulmonology / Airway disease
Sex & age distribution: Male: affected, 8:1 male predominance; Female: affected; Children: rare
Gene(s) involved: None recorded

Etiology & mechanism

Elastic and smooth muscle atrophy of tracheal wall.

Gene(s) involved (0)

No gene recorded.

Symptoms & signs (5)

bronchiectasischronic coughdyspneahemoptysisrecurrent lower respiratory infection

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