Kawasaki syndrome

Also known as: Mucocutaneous lymph node syndrome

Acute medium-vessel vasculitis of early childhood.

Medical specialty: Pediatrics
Subspecialty: Pediatrics / Pediatric rheumatology
Sex & age distribution: Male: affected, 1.5:1 male predominance; Female: affected; Children: yes, mostly under 5 years
Gene(s) involved: CASP3, FCGR2A, ITPKC, ORAI1

Etiology & mechanism

Immune-mediated vasculitis with coronary artery aneurysm risk.

Gene(s) involved (4)

CASP3FCGR2AITPKCORAI1

Symptoms & signs (7)

cervical lymphadenopathyconjunctival injectioncoronary aneurysmshand and foot edemapersistent feverrashstrawberry tongue

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