🧬 SyndromeScope
Syndrome reference sheet
Generated 13 Oct 2026
Neurology · Neurology / Epilepsy; Pediatric neurology Hemiconvulsion–hemiplegia–epilepsy syndrome
Also known as: HHE
Prolonged hemiconvulsion followed by hemiplegia and later epilepsy.
- Medical specialty
- Neurology
- Subspecialty
- Neurology / Epilepsy; Pediatric neurology
- Sex & age distribution
- Male: affected; Female: affected; Children: yes, mainly children under 4 years
- Gene(s) involved
- None recorded
Etiology & mechanism
Febrile status with hemispheric injury.
Gene(s) involved (0)
No gene recorded.
Symptoms & signs (3)
epilepsyhemiconvulsionshemiplegia