Glucagonoma syndrome

Also known as: Necrolytic migratory erythema syndrome

Glucagon-secreting tumor with characteristic rash and diabetes.

Medical specialty: Endocrinology
Subspecialty: Endocrinology / Neuroendocrine tumors
Sex & age distribution: Male: affected; Female: affected; Children: rare
Gene(s) involved: MEN1

Etiology & mechanism

Pancreatic alpha-cell tumor.

Gene(s) involved (1)

MEN1

Symptoms & signs (7)

anemiadiabetesdiarrheanecrolytic migratory erythemastomatitisthrombosisweight loss

SyndromeScope — educational reference. Content is model-generated and not clinically verified; always confirm against OMIM, Orphanet and GeneReviews before clinical use.