Febrile infection-related epilepsy syndrome

Also known as: FIRES

Devastating epileptic encephalopathy with refractory status epilepticus after a febrile illness.

Medical specialty: Neurology
Subspecialty: Neurology / Epilepsy; Neurocritical care
Sex & age distribution: Male: slightly more common; Female: affected; Children: yes, school-age children mostly
Gene(s) involved: None recorded

Etiology & mechanism

Cause unknown; presumed inflammatory.

Gene(s) involved (0)

No gene recorded.

Symptoms & signs (4)

chronic epilepsycognitive impairmentfeverrefractory status epilepticus

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