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Syndrome reference sheet
Generated 12 Oct 2026
Neurology · Neurology / Neuro-oncology Bing–Neel syndrome
Also known as: Bing–Neel
CNS involvement of Waldenström macroglobulinemia.
- Medical specialty
- Neurology
- Subspecialty
- Neurology / Neuro-oncology
- Sex & age distribution
- Male: affected, more common; Female: affected; Children: no
- Gene(s) involved
- MYD88
Etiology & mechanism
Lymphoplasmacytic infiltration.
Gene(s) involved (1)
MYD88
Symptoms & signs (3)
cognitive changecranial neuropathymotor deficits